Unusual presentation of childhood Systemic Lupus Erythematosus
نویسندگان
چکیده
Bullous systemic lupus erythematosus is a rare blistering condition with a distinctive combination of clinical, histological and immunopathologic features that together constitute a unique bullous disease phenotype. It is often associated with autoimmunity to type VII collagen. Here we report a child who presented with bullous systemic lupus erythematosus. Rapid resolution of the blisters occurred following treatment with dapsone.
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عنوان ژورنال:
- Pediatric Rheumatology Online Journal
دوره 5 شماره
صفحات -
تاریخ انتشار 2007